Oligodontia of Permanent Dentition: Case Reports

ALİ RIZA ALPÖZ, ÇİĞDEM ELBEK, ÖZANTÖNÇAG
Ege University, Faculty of Dentistry, Department of Paedodontics, Bornova 35100, İzmir, TURKEY

SUMMARY
Oligodontia is defined as congenital absence of 6 or more teeth, excluding the third molars. Genetic factors play an important role in the aetiology of oligodontia, which can occur as an isolated finding (Oligodontia I) or as part of a syndrome (Oligodontia S). Characteristic dental symptoms are a reduced mımber of teeth, reduction in tooth size, anomalies oftooth form and delayed eruption.
This article presents 3 cases of relatives (sister, brother and a cousin) with oligodontia. Sister and brother's family had a consanguineous marriage. While sister (case I) had an associated familial Mediterranean fever (FMF), no FMF were found in other cases.